2-Methylsuccinic acid [498-21-5]

TargetMol Chemicals

2-Methylsuccinic acid

4

498-21-5

Chemical

Research Use Only

2-Methylsuccinic acid

98%

C5H8O4

132.115

2-Methylsuccinic acid (Pyrotartaric Acid) is a normal metabolite found in human fluids. Increased urinary levels of 2-Methylsuccinic acid (Pyrotartaric Acid) (together with ethylmalonic acid) are the main biochemical measurable features in ethylmalonic encephalopathy, a rare metabolic disorder with an autosomal recessive mode of inheritance that is clinically characterized by neuromotor delay, hyperlactic acidemia, recurrent petechiae, orthostatic acrocyanosis, and chronic diarrhea.

3 years

CC(CC(O)=O)C(O)=O

-20°C

12352200