ASS1 Polyclonal Antibody
RD252452A
ApplicationsWestern Blot, ELISA
Product group Antibodies
ReactivityHuman, Mouse, Rat
TargetASS1
Overview
- SupplierReddot Biotech
- Product NameASS1 Polyclonal Antibody
- Delivery Days Customer5
- ApplicationsWestern Blot, ELISA
- CertificationResearch Use Only
- ClonalityPolyclonal
- Concentration0.4 mg/ml
- ConjugateUnconjugated
- Gene ID445
- Target nameASS1
- Target descriptionargininosuccinate synthase 1
- Target synonymsargininosuccinate synthase; argininosuccinate synthetase 1; ASS; citrulline-aspartate ligase; CTLN1; epididymis secretory sperm binding protein
- HostRabbit
- IsotypeIgG
- Scientific DescriptionASS1 is a rate-limiting enzyme in the urea cycle. Citrullinemia type I is an autosomal recessive disorder that is caused by a deficiency of the urea cycle enzyme argininosuccinate synthetase (ASS1). Deficiency of ASS1 shows various clinical manifestations encompassing severely affected patients with fatal neonatal hyperammonemia as well as asymptomatic individuals with only a biochemical phenotype.
- ReactivityHuman, Mouse, Rat
- Storage Instruction-20°C
- UNSPSC12352203