DYSF Antibody, FITC conjugated
CSB-PA007314LC01HU
ReactivityHuman
Product group Antibodies
TargetDYSF
Overview
- SupplierCusabio
- Product NameDYSF Antibody, FITC conjugated
- Delivery Days Customer20
- CertificationResearch Use Only
- ClonalityPolyclonal
- ConjugateFITC
- Gene ID8291
- Target nameDYSF
- Target descriptiondysferlin
- Target synonymsdysferlin; dystrophy-associated fer-1-like 1; FER1L1; fer-1-like family member 1; fer-1-like protein 1; LGMD2B; LGMDR2; limb girdle muscular dystrophy 2B (autosomal recessive); MMD1
- HostRabbit
- IsotypeIgG
- Protein IDO75923
- Protein NameDysferlin
- Scientific DescriptionKey calcium ion sensor involved in the Ca(2+)-triggered synaptic vesicle-plasma membrane fusion. Plays a role in the sarcolemma repair mechanism of both skeletal muscle and cardiomyocytes that permits rapid resealing of membranes disrupted by mechanical stress (By similarity).
- ReactivityHuman
- Storage Instruction-20°C or -80°C
- UNSPSC12352203