GLB1 antibody

GeneTex

GLB1 antibody

9

Western Blot

Research Use Only

Polyclonal

0.87 mg/ml

Unconjugated

Glb1

galactosidase, beta 1

acid beta-galactosidase; AW125515; beta-galactosidase; Bg; Bge; Bgl; Bgl-; Bgl-e; Bgl-s; Bgl-t; Bgs; Bgt; C130097A14Rik; lactase

Rabbit

IgG

This gene encodes a preproprotein that is proteolytically cleaved to yield a signal peptide and a proproptein that is subsequently processed to generate the active mature peptide. The encoded protein is a lysosomal enzyme that catalyzes the hydrolysis of terminal beta-D-galactose residues in various substrates like lactose, ganglioside GM1 and other glycoproteins. Mutations in the human gene are associated with GM1-gangliosidosis and Morquio B syndrome. Disruption of the mouse gene mirrors the symptoms of human gangliosidosis. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Dec 2013]

Mouse, Rat

2°C to 8°C,-20°C or -80°C

12352203