GM2A Polyclonal Antibody
RD267777A
ApplicationsWestern Blot
Product group Antibodies
ReactivityMouse, Rat
TargetGM2A
Overview
- SupplierReddot Biotech
- Product NameGM2A Polyclonal Antibody
- Delivery Days Customer5
- ApplicationsWestern Blot
- CertificationResearch Use Only
- Concentration1 mg/ml
- ConjugateUnconjugated
- Gene ID2760
- Target nameGM2A
- Target descriptionGM2 ganglioside activator
- Target synonymscerebroside sulfate activator protein; ganglioside GM2 activator; GM2-AP; SAP-3; shingolipid activator protein 3; sphingolipid activator protein 3
- HostRabbit
- IsotypeIgG
- Scientific DescriptionThis gene encodes a small glycolipid transport protein which acts as a substrate specific co-factor for the lysosomal enzyme beta-hexosaminidase A. Beta-hexosaminidase A, together with GM2 ganglioside activator, catalyzes the degradation of the ganglioside GM2, and other molecules containing terminal N-acetyl hexosamines. Mutations in this gene result in GM2-gangliosidosis type AB or the AB variant of Tay-Sachs disease. Alternative splicing results in multiple transcript variants.
- ReactivityMouse, Rat
- Storage Instruction-20°C
- UNSPSC12352203