Anti-delta Sarcoglycan Antibody [JM61-10]
ET1703-88
ApplicationsImmunoPrecipitation, Western Blot, ImmunoHistoChemistry, ImmunoHistoChemistry Paraffin
Product group Antibodies
ReactivityHuman
TargetSGCD
Overview
- SupplierHUABIO
- Product NameAnti-delta Sarcoglycan Antibody [JM61-10]
- Delivery Days Customer7
- ApplicationsImmunoPrecipitation, Western Blot, ImmunoHistoChemistry, ImmunoHistoChemistry Paraffin
- Applications SupplierWB,IP,IHC-P
- CertificationResearch Use Only
- ClonalityMonoclonal
- Clone IDJM61-10
- Concentration1 mg/ml
- ConjugateUnconjugated
- Gene ID6444
- Target nameSGCD
- Target descriptionsarcoglycan delta
- Target synonyms35DAG, CMD1L, DAGD, LGMDR6, SG-delta, SGCDP, SGD, delta-sarcoglycan, 35 kDa dystrophin-associated glycoprotein, delta-SG, dystrophin associated glycoprotein, delta sarcoglycan, placental delta sarcoglycan, sarcoglycan, delta (35kDa dystrophin-associated glycoprotein)
- HostRabbit
- IsotypeIgG
- Protein IDQ92629
- Protein NameDelta-sarcoglycan
- Scientific DescriptionComponent of the sarcoglycan complex, a subcomplex of the dystrophin-glycoprotein complex which forms a link between the F-actin cytoskeleton and the extracellular matrix. Defects in SGCD are the cause of limb-girdle muscular dystrophy type 2F (LGMD2F) [MIM:601287]. LGMD2F is an autosomal recessive disorder. Defects in SGCD are the cause of cardiomyopathy dilated type 1L (CMD1L) [MIM:606685]. Dilated cardiomyopathy is a disorder characterized by ventricular dilation and impaired systolic function, resulting in congestive heart failure and arrhythmia. Patients are at risk of premature death.
- ReactivityHuman
- Reactivity SupplierHuman
- Storage Instruction-20°C,2°C to 8°C
- UNSPSC41116161