Anti-GAA Antibody [JE54-59]
ET7110-77
ApplicationsImmunoFluorescence, Western Blot, ImmunoHistoChemistry, ImmunoHistoChemistry Paraffin
Product group Antibodies
ReactivityHuman
TargetGAA
Overview
- SupplierHUABIO
- Product NameAnti-GAA Antibody [JE54-59]
- Delivery Days Customer7
- ApplicationsImmunoFluorescence, Western Blot, ImmunoHistoChemistry, ImmunoHistoChemistry Paraffin
- Applications SupplierWB,IF-Tissue,IHC-P,FC
- CertificationResearch Use Only
- ClonalityMonoclonal
- Clone IDJE54-59
- Concentration1 mg/ml
- ConjugateUnconjugated
- Gene ID2548
- Target nameGAA
- Target descriptionalpha glucosidase
- Target synonymsIOPD, LOPD, LYAG, lysosomal alpha-glucosidase, acid maltase, aglucosidase alfa, glucosidase alpha, acid
- HostRabbit
- IsotypeIgG
- Protein IDP10253
- Protein NameLysosomal alpha-glucosidase
- Scientific DescriptionThis gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II, also known as Pompes disease, which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants.
- ReactivityHuman
- Reactivity SupplierHuman
- Storage Instruction-20°C,2°C to 8°C
- UNSPSC41116161