Anti-GBA Antibody [JM10-76]

HUABIO

Anti-GBA Antibody [JM10-76]

7

Western Blot, ImmunoHistoChemistry, ImmunoHistoChemistry Paraffin

WB,IHC-P

Research Use Only

Monoclonal

JM10-76

1 mg/ml

Unconjugated

GBA1

glucosylceramidase beta 1

GBA, GCB, GLUC, lysosomal acid glucosylceramidase, D-glucosyl-N-acylsphingosine glucohydrolase, SGTase, acid beta-glucosidase, alglucerase, beta-GC, beta-glucocerebrosidase, beta-glucosylceramidase 1, cholesterol glucosyltransferase, cholesteryl-beta-glucosidase, glucocerebrosidase, glucosidase, beta, acid, glucosylceramidase-like protein, imiglucerase, lysosomal acid GCase, lysosomal cholesterol glycosyltransferase, lysosomal galactosylceramidase, lysosomal glucocerebrosidase, lysosomal glycosylceramidase

Rabbit

IgG

Lysosomal acid glucosylceramidase

beta-Glucosidase is a predominantly liver enzyme which efficiently hydrolyzes beta-D-glucoside and beta-D-galactoside. Defects in beta-glucosidase cause Gaucher disease, an inherited condition distinguished by the accumulation of glucosylceramide within the cells of the reticuloendothelial system. beta-Glucosidase is used in enzyme replacement treatment aimed at treating Gaucher disease. The absorption of dietary flavonoid glycosides in humans involves a critical deglycosylation step that is mediated by epithelial beta-glucosidases.

Human, Mouse, Rat

Human,Mouse,Rat

-20°C,2°C to 8°C

41116161