BCS1L Antibody

Aviva Systems Biology

BCS1L Antibody

23

WB: 1:500~2000 IHC: 1:50~200

Western Blot, ImmunoHistoChemistry

Research Use Only

Polyclonal

Unconjugated

Liquid. PBS with 0.02% sodium azide, 50% glycerol, pH 7.3

BCS1L

BCS1 ubiquinol-cytochrome c reductase complex chaperone

BCS, BCS1, BJS, FLNMS, GRACILE, Hs.6719, MC3DN1, PTD, h-BCS, h-BCS1, mitochondrial chaperone BCS1, BC1 (ubiquinol-cytochrome c reductase) synthesis-like, BCS1 homolog, ubiquinol-cytochrome c reductase complex chaperone, BCS1-like protein, mitochondrial complex III assembly

Rabbit

IgG

Mitochondrial chaperone BCS1

This gene encodes a homolog of the S. cerevisiae bcs1 protein which is involved in the assembly of complex III of the mitochondrial respiratory chain. The encoded protein does not contain a mitochondrial targeting sequence but experimental studies confirm that it is imported into mitochondria. Mutations in this gene are associated with mitochondrial complex III deficiency and the GRACILE syndrome. Several alternatively spliced transcripts encoding two different isoforms have been described.

Human, Mouse, Rat

-20°C

41116161