BCS1L Polyclonal Antibody

Reddot Biotech

BCS1L Polyclonal Antibody

5

ImmunoFluorescence, ImmunoHistoChemistry

Research Use Only

1 mg/ml

Unconjugated

BCS1L

BCS1 homolog, ubiquinol-cytochrome c reductase complex chaperone

BC1 (ubiquinol-cytochrome c reductase) synthesis-like; BCS; BCS1; BCS1-like protein; BJS; FLNMS; GRACILE; h-BCS; h-BCS1; Hs.6719; MC3DN1; mitochondrial chaperone BCS1; mitochondrial complex III assembly; PTD

Rabbit

IgG

This gene encodes a homolog of the S. cerevisiae bcs1 protein which is involved in the assembly of complex III of the mitochondrial respiratory chain. The encoded protein does not contain a mitochondrial targeting sequence but experimental studies confirm that it is imported into mitochondria. Mutations in this gene are associated with mitochondrial complex III deficiency and the GRACILE syndrome. Several alternatively spliced transcripts encoding two different isoforms have been described.

-20°C

12352203