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Immunofluorescent analysis of A549 cells using CSB-PA00395A0Rb at dilution of 1:100 and Alexa Fluor 488-congugated AffiniPure Goat Anti-Rabbit IgG(H+L)
Immunofluorescent analysis of A549 cells using CSB-PA00395A0Rb at dilution of 1:100 and Alexa Fluor 488-congugated AffiniPure Goat Anti-Rabbit IgG(H+L)
Immunofluorescent analysis of A549 cells using CSB-PA00395A0Rb at dilution of 1:100 and Alexa Fluor 488-congugated AffiniPure Goat Anti-Rabbit IgG(H+L)

COX6B1 Antibody

CSB-PA00395A0RB
Cusabio
ApplicationsImmunoFluorescence, ELISA
Product group Antibodies
ReactivityHuman
TargetCOX6B1
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Overview

  • Supplier
    Cusabio
  • Product Name
    COX6B1 Antibody
  • Delivery Days Customer
    20
  • Applications
    ImmunoFluorescence, ELISA
  • Certification
    Research Use Only
  • Clonality
    Polyclonal
  • Conjugate
    Unconjugated
  • Gene ID1340
  • Target name
    COX6B1
  • Target description
    cytochrome c oxidase subunit 6B1
  • Target synonyms
    COX6B, COXG, COXVIb1, MC4DN7, cytochrome c oxidase subunit 6B1, COX VIb-1, cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous)
  • Host
    Rabbit
  • Isotype
    IgG
  • Protein IDP14854
  • Protein Name
    Cytochrome c oxidase subunit 6B1
  • Scientific Description
    Defects in COX6B1 are a cause of mitochondrial complex IV deficiency (MT-C4D) [MIM:220110]; also known as cytochrome c oxidase deficiency. A disorder of the mitochondrial respiratory chain with heterogeneous clinical manifestations, ranging from isolated myopathy to severe multisystem disease affecting several tissues and organs. Features include hypertrophic cardiomyopathy, hepatomegaly and liver dysfunction, hypotonia, muscle weakness, excercise intolerance, developmental delay, delayed motor development and mental retardation. A subset of patients manifest Leigh syndrome.
  • Reactivity
    Human
  • Storage Instruction
    -20°C or -80°C
  • UNSPSC
    41116161