
Immunohistochemistry of paraffin-embedded human skeletal muscle tissue using CSB-PA007314LA01HU at dilution of 1:100
DYSF Antibody
CSB-PA007314LA01HU
ApplicationsImmunoFluorescence, ELISA, ImmunoHistoChemistry
Product group Antibodies
ReactivityHuman
TargetDYSF
Overview
- SupplierCusabio
- Product NameDYSF Antibody
- Delivery Days Customer20
- ApplicationsImmunoFluorescence, ELISA, ImmunoHistoChemistry
- CertificationResearch Use Only
- ClonalityPolyclonal
- ConjugateUnconjugated
- Gene ID8291
- Target nameDYSF
- Target descriptiondysferlin
- Target synonymsFER1L1, LGMD2B, LGMDR2, MMD1, dysferlin, dystrophy-associated fer-1-like 1, fer-1-like family member 1, fer-1-like protein 1, limb girdle muscular dystrophy 2B (autosomal recessive)
- HostRabbit
- IsotypeIgG
- Protein IDO75923
- Protein NameDysferlin
- Scientific DescriptionKey calcium ion sensor involved in the Ca(2+)-triggered synaptic vesicle-plasma membrane fusion. Plays a role in the sarcolemma repair mechanism of both skeletal muscle and cardiomyocytes that permits rapid resealing of membranes disrupted by mechanical stress (By similarity).
- ReactivityHuman
- Storage Instruction-20°C or -80°C
- UNSPSC41116161






