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WB analysis of various sample lysates using GTX64809 ETHE1 antibody. Dilution : 1:1000 Loading : 25microg per lane
WB analysis of various sample lysates using GTX64809 ETHE1 antibody. Dilution : 1:1000 Loading : 25microg per lane
WB analysis of various sample lysates using GTX64809 ETHE1 antibody. Dilution : 1:1000 Loading : 25microg per lane

ETHE1 antibody

GTX64809
GeneTex
ApplicationsImmunoFluorescence, Western Blot, ImmunoCytoChemistry, ImmunoHistoChemistry, ImmunoHistoChemistry Paraffin
Product group Antibodies
TargetETHE1
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Overview

  • Supplier
    GeneTex
  • Product Name
    ETHE1 antibody
  • Delivery Days Customer
    9
  • Application Supplier Note
    WB: 1:200 - 1:1000. ICC/IF: 1:50 - 1:200. IHC-P: 1:50 - 1:200. *Optimal dilutions/concentrations should be determined by the researcher.Not tested in other applications.
  • Applications
    ImmunoFluorescence, Western Blot, ImmunoCytoChemistry, ImmunoHistoChemistry, ImmunoHistoChemistry Paraffin
  • Certification
    Research Use Only
  • Clonality
    Polyclonal
  • Conjugate
    Unconjugated
  • Gene ID23474
  • Target name
    ETHE1
  • Target description
    ETHE1 persulfide dioxygenase
  • Target synonyms
    ethylmalonic encephalopathy 1; hepatoma subtracted clone one protein; HSCO; persulfide dioxygenase ETHE1, mitochondrial; protein ETHE1, mitochondrial; sulfur dioxygenase ETHE1; YF13H12
  • Host
    Rabbit
  • Isotype
    IgG
  • Protein IDO95571
  • Protein Name
    Persulfide dioxygenase ETHE1, mitochondrial
  • Scientific Description
    This gene encodes a member of the metallo beta-lactamase family of iron-containing proteins involved in the mitochondrial sulfide oxidation pathway. The encoded protein catalyzes the oxidation of a persulfide substrate to sulfite. Certain mutations in this gene cause ethylmalonic encephalopathy, an infantile metabolic disorder affecting the brain, gastrointestinal tract and peripheral vessels. Alternative splicing results in multiple transcript variants encoding different isoforms. [provided by RefSeq, Mar 2016]
  • Storage Instruction
    -20°C or -80°C,2°C to 8°C
  • UNSPSC
    12352203

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