![Globotriaosylceramides (porcine) [71965-57-6] Globotriaosylceramides (porcine) [71965-57-6]](https://www.targetmol.com/group3/M00/02/FA/CgoaEWY7PjSEHRHaAAAAAJuNErE878.png)
Globotriaosylceramides (porcine) [71965-57-6]
T36186
Overview
- SupplierTargetMol Chemicals
- Product NameGlobotriaosylceramides (porcine) [71965-57-6]
- Delivery Days Customer16
- CAS Number71965-57-6
- Category SupplierChemical
- CertificationResearch Use Only
- Chemical NameGlobotriaosylceramides (porcine)
- Molecular FormulaC60H113NO18
- Molecular Weight1136.553
- Scientific DescriptionGlobotriaosycleramides are glycosphingolipids found in mammalian cell membranes that are synthesized from lactosylceramides . They act as receptors for Shiga and Shiga-like toxins in vitro and in vivo. Globotriaosylceramides accumulate in endothelial cells, pericytes, vascular smooth muscle cells, renal epithelial cells, dorsal ganglia neuronal cells, and myocardial cells in patients with Fabry disease, a lysosomal storage disorder characterized by a deficiency in the enzyme alpha-galactosidase A. Globotriaosylceramides act as natural resistance factors to HIV infection, interacting with HIV gp120 to prevent its interaction with chemokine co-receptors and subsequent fusion of HIV to host cell membranes. This product contains a mixture of hydroxy and non-hydroxy fatty acid-containing globotriaosylceramides isolated from porcine red blood cells (RBCs).
- Shelf life instruction3 years
- SMILESCCCCCCCCCCCCCCCCCCCCCCCC(=O)N[C@@H](CO[C@@H]1O[C@H](CO)[C@@H](O[C@@H]2O[C@H](CO)[C@H](O[C@H]3O[C@H](CO)[C@H](O)[C@H](O)[C@H]3O)[C@H](O)[C@H]2O)[C@H](O)[C@H]1O)[C@H](O)\C=C\CCCCCCCCCCCCC
- Storage Instruction-20°C
- UNSPSC12352200