OTC antibody

GeneTex

OTC antibody

9

WB: 1:1000 - 1:4000. IHC-P: 1:50 - 1:100. *Optimal dilutions/concentrations should be determined by the researcher.Not tested in other applications.

Western Blot, ImmunoHistoChemistry, ImmunoHistoChemistry Paraffin

Research Use Only

Polyclonal

Unconjugated

OTC

ornithine transcarbamylase

OCTD, OTC1, OTCD, OTCase, ornithine transcarbamylase, mitochondrial, ornithine carbamoyltransferase, mitochondrial

Rabbit

IgG

Ornithine carbamoyltransferase, mitochondrial

This nuclear gene encodes a mitochondrial matrix enzyme. Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia. Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also. [provided by RefSeq, Jul 2008]

-20°C or -80°C,2°C to 8°C

12352203