Western blot analysis of extracts of various cell lines using PEX3 Polyclonal Antibody at 1:1000 dilution.
Western blot analysis of extracts of various cell lines using PEX3 Polyclonal Antibody at 1:1000 dilution.
PEX3 Polyclonal Antibody
E-AB-62971
Product group Antibodies
Overview
- SupplierElabscience
- Product NamePEX3 Polyclonal Antibody
- Delivery Days Customer12
- CertificationResearch Use Only
- Scientific DescriptionThe product of this gene is involved in peroxisome biosynthesis and integrity. It assembles membrane vesicles before the matrix proteins are translocated. Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. The peroxisomal biogenesis disorders are a heterogeneous group with at least 14 complementation groups and with more than 1 phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause Zellweger syndrome (ZWS).
- UNSPSC12352203