SGSH antibody [N1N3]

GeneTex

SGSH antibody [N1N3]

9

WB: 1:500-1:3000. *Optimal dilutions/concentrations should be determined by the researcher.Not tested in other applications.

Western Blot

Research Use Only

Polyclonal

2 mg/ml

Unconjugated

SGSH

N-sulfoglucosamine sulfohydrolase

heparan sulfate sulfatase; HSS; MPS3A; mucopolysaccharidosis type IIIA; N-sulphoglucosamine sulphohydrolase; SFMD; sulfoglucosamine sulfamidase; sulphamidase

Rabbit

IgG

N-sulphoglucosamine sulphohydrolase

This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. [provided by RefSeq]

Human

-20°C or -80°C,2°C to 8°C

12352203