SURF1 antibody [N2C3]

GeneTex

SURF1 antibody [N2C3]

9

WB: 1:500-1:3000. *Optimal dilutions/concentrations should be determined by the researcher.Not tested in other applications.

Western Blot

Research Use Only

Polyclonal

0.83 mg/ml

Unconjugated

SURF1

SURF1 cytochrome c oxidase assembly factor

CMT4K; MC4DN1; SHY1; surfeit 1; surfeit locus protein 1

Rabbit

IgG

Surfeit locus protein 1

This gene encodes a protein localized to the inner mitochondrial membrane and thought to be involved in the biogenesis of the cytochrome c oxidase complex. The protein is a member of the SURF1 family, which includes the related yeast protein SHY1 and rickettsial protein RP733. The gene is located in the surfeit gene cluster, a group of very tightly linked genes that do not share sequence similarity, where it shares a bidirectional promoter with SURF2 on the opposite strand. Defects in this gene are a cause of Leigh syndrome, a severe neurological disorder that is commonly associated with systemic cytochrome c oxidase deficiency. [provided by RefSeq]

Human

-20°C or -80°C,2°C to 8°C

12352203