Telethonin antibody [N1C3]

GeneTex

Telethonin antibody [N1C3]

9

WB: 1:500-1:3000. IHC-P: 1:100-1:1000. *Optimal dilutions/concentrations should be determined by the researcher.Not tested in other applications.

Western Blot, ImmunoHistoChemistry, ImmunoHistoChemistry Paraffin

Research Use Only

Polyclonal

1 mg/ml

Unconjugated

TCAP

titin-cap

CMD1N, CMH25, LGMD2G, LGMDR7, T-cap, TELE, telethonin, telethonin, 19 kDa sarcomeric protein, limb girdle muscular dystrophy 2G (autosomal recessive), teneurin C-terminal associated peptide, titin cap protein

Rabbit

IgG

Telethonin

Sarcomere assembly is regulated by the muscle protein titin. Titin is a giant elastic protein with kinase activity that extends half the length of a sarcomere. It serves as a scaffold to which myofibrils and other muscle related proteins are attached. This gene encodes a protein found in striated and cardiac muscle that binds to the titin Z1-Z2 domains and is a substrate of titin kinase, interactions thought to be critical to sarcomere assembly. Mutations in this gene are associated with limb-girdle muscular dystrophy type 2G. [provided by RefSeq, Jul 2008]

Human, Mouse

-20°C or -80°C,2°C to 8°C

41116161