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DAG1 / beta Dystroglycan antibody [C2C3-2], C-term

Research Use Only
GTX124225
GeneTex
ApplicationsImmunoFluorescence, Western Blot, ImmunoCytoChemistry, ImmunoHistoChemistry, ImmunoHistoChemistry Paraffin
Product group Antibodies
ReactivityHuman, Mouse
TargetDAG1
Price on request
Packing Size
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Overview

  • Supplier
    GeneTex
  • Product Name
    DAG1 / beta Dystroglycan antibody [C2C3-2], C-term
  • Delivery Days Customer
    9
  • Applications
    ImmunoFluorescence, Western Blot, ImmunoCytoChemistry, ImmunoHistoChemistry, ImmunoHistoChemistry Paraffin
  • Certification
    Research Use Only
  • Clonality
    Polyclonal
  • Concentration
    0.6 mg/ml
  • Conjugate
    Unconjugated
  • Gene ID1605
  • Target name
    DAG1
  • Target description
    dystroglycan 1
  • Target synonyms
    156DAG; A3a; AGRNR; DAG; dystroglycan; dystroglycan 1 (dystrophin-associated glycoprotein 1); LGMDR16; MDDGA9; MDDGC7; MDDGC9
  • Host
    Rabbit
  • Isotype
    IgG
  • Scientific Description
    Dystroglycan is a laminin binding component of the dystrophin-glycoprotein complex which provides a linkage between the subsarcolemmal cytoskeleton and the extracellular matrix. Dystroglycan 1 is a candidate gene for the site of the mutation in autosomal recessive muscular dystrophies. The dramatic reduction of dystroglycan 1 in Duchenne muscular dystrophy leads to a loss of linkage between the sarcolemma and extracellular matrix, rendering muscle fibers more susceptible to necrosis. Dystroglycan also functions as dual receptor for agrin and laminin-2 in the Schwann cell membrane. The muscle and nonmuscle isoforms of dystroglycan differ by carbohydrate moieties but not protein sequence. [provided by RefSeq]
  • Reactivity
    Human, Mouse
  • Storage Instruction
    2°C to 8°C,-20°C or -80°C
  • UNSPSC
    12352203

References

  • GMPPA defects cause a neuromuscular disorder with alpha-dystroglycan hyperglycosylation. Franzka P et al., 2021 May 3, J Clin Invest
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  • The Association Between beta-Dystroglycan in Airway Smooth Muscle and Eosinophils in Allergic Asthma. Shareef SH et al., 2021 Jun, Inflammation
    Read more