PCCA antibody

GeneTex

PCCA antibody

9

WB: 1:1000 - 1:3000. *Optimal dilutions/concentrations should be determined by the researcher.Not tested in other applications.

Western Blot

Research Use Only

Polyclonal

Unconjugated

PCCA

propionyl-CoA carboxylase subunit alpha

pccA complementation group; PCCase alpha subunit; propanoyl-CoA:carbon dioxide ligase alpha subunit; propionyl CoA carboxylase, alpha polypeptide; propionyl Coenzyme A carboxylase, alpha polypeptide; propionyl-CoA carboxylase alpha chain, mitochondrial; propionyl-CoA carboxylase alpha subunit

Rabbit

IgG

Propionyl-CoA carboxylase alpha chain, mitochondrial

The protein encoded by this gene is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA encodes the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia. Multiple transcript variants encoding different isoforms have been found for this gene.[provided by RefSeq, May 2010]

-20°C or -80°C,2°C to 8°C

12352203