Bio-Connect

NBS1 antibody [1D7]

GTX70224
GeneTex
ApplicationsImmunoFluorescence, ImmunoPrecipitation, Western Blot, ImmunoCytoChemistry
Product group Antibodies
ReactivityHuman, Mouse, Rat
TargetNBN
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Overview

  • Supplier
    GeneTex
  • Product Name
    NBS1 antibody [1D7] - KO/KD Validated
  • Delivery Days Customer
    9
  • Application Supplier Note
    WB: 1:500-1:3000. ICC/IF: 1:100. *Optimal dilutions/concentrations should be determined by the researcher.Not tested in other applications.
  • Applications
    ImmunoFluorescence, ImmunoPrecipitation, Western Blot, ImmunoCytoChemistry
  • Certification
    Research Use Only
  • Clonality
    Monoclonal
  • Clone ID
    1D7
  • Concentration
    1 mg/ml
  • Conjugate
    Unconjugated
  • Gene ID4683
  • Target name
    NBN
  • Target description
    nibrin
  • Target synonyms
    ATV; AT-V1; AT-V2; cell cycle regulatory protein p95; NBS; NBS1; nibrin; Nijmegen breakage syndrome 1 (nibrin); P95; p95 protein of the MRE11/RAD50 complex
  • Host
    Mouse
  • Isotype
    IgG1
  • Protein IDO60934
  • Protein Name
    Nibrin
  • Scientific Description
    Mutations in this gene are associated with Nijmegen breakage syndrome, an autosomal recessive chromosomal instability syndrome characterized by microcephaly, growth retardation, immunodeficiency, and cancer predisposition. The encoded protein is a member of the MRE11/RAD50 double-strand break repair complex which consists of 5 proteins. This gene product is thought to be involved in DNA double-strand break repair and DNA damage-induced checkpoint activation. [provided by RefSeq, Jul 2008]
  • Reactivity
    Human, Mouse, Rat
  • Storage Instruction
    -20°C or -80°C,2°C to 8°C
  • UNSPSC
    12352203

References

  • Widespread BRCA1/2-independent homologous recombination defects are caused by alterations in RNA-binding proteins.
    Read more
  • Pathogenic variants in SLF2 and SMC5 cause segmented chromosomes and mosaic variegated hyperploidy.
    Read more
  • Increased Resection at DSBs in G(2)-Phase Is a Unique Phenotype Associated with DNA-PKcs Defects That Is Not Shared by Other Factors of c-NHEJ. Xiao H et al., 2022 Jul 2, Cells
    Read more
  • 53BP1-mediated recruitment of RASSF1A to ribosomal DNA breaks promotes local ATM signaling. Tsaridou S et al., 2022 Aug 3, EMBO Rep
    Read more
  • Chemical screen identifies shikonin as a broad DNA damage response inhibitor that enhances chemotherapy through inhibiting ATM and ATR. Wang F et al., 2022 Mar, Acta Pharm Sin B
    Read more
  • A Single Amino Acid Switch in the Adenoviral DNA Binding Protein Abrogates Replication Center Formation and Productive Viral Infection. Boddin J et al., 2022 Apr 26, mBio
    Read more
  • RECON syndrome is a genome instability disorder caused by mutations in the DNA helicase RECQL1. Abu-Libdeh B et al., 2022 Mar 1, J Clin Invest
    Read more
  • RAD50 Loss of Function Variants in the Zinc Hook Domain Associated with Higher Risk of Familial Esophageal Squamous Cell Carcinoma. Ko JMY et al., 2021 Sep 21, Cancers (Basel)
    Read more
  • Radiosensitization Effect of AGuIX, a Gadolinium-Based Nanoparticle, in Nonsmall Cell Lung Cancer. Du Y et al., 2020 Dec 23, ACS Appl Mater Interfaces
    Read more
  • NBS1 interacts with Notch signaling in neuronal homeostasis. Zhou ZW et al., 2020 Nov 4, Nucleic Acids Res
    Read more